What is Desmoplastic small round cell tumors?

Desmoplastic small round cell tumors (DSRCT) are a type of soft-tissue sarcoma. DSRCT causes multiple tumors to form in the abdomen and pelvis area, but exactly where it begins usually is not known.

The disease is most common in Caucasian boys. Although researchers think a problem with the genes may cause DSRCT, this has not been proven.

Since DSRCT often is not diagnosed until the cancer is advanced, tumors grow large and spread through the lymph system or blood stream to other parts of the body. They can spread to many areas of the body, including the lymph nodes, lungs, bone and liver. Other types of cancer, including rhabdomyosarcoma, may be in the abdomen as well.

DSRCT is a dangerous type of cancer that often is resistant to treatment and frequently comes back after treatment.

In rare cases, DSRCT may be passed down from one generation to the next. Genetic counseling may be right for you. Visit our genetic testing page to learn more.

Why Choose us for your treatment ?

A team of highly focused renowned physicians, including surgeons, oncologists and radiologists, as well as a specialized support staff of nurses, physician’s assistants and others follow your child from diagnosis through treatment.
DSRCT often is difficult to diagnose. ACH utilizes the most advanced technology and techniques to pinpoint the cancer.

HIPEC (hyperthermic peritoneal perfusion with chemotherapy) which was pioneered at ACH combines surgery with heated chemotherapy for a safe and often effective treatment. It has been shown to extend survival time in many patients.

ACH is designed just for children, with a full range of services and amenities that help make the child and family’s experience as comfortable as possible. We go beyond medical care to deliver a comprehensive experience that treats the whole child.